產品型號:K106618P
更新時間:2022-08-15
廠商性質:生產廠家
訪 問 量 :889
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產品分類
Anti-HADHA Polyclonal Antibody
英文名稱 | Anti-HADHA Polyclonal Antibody |
---|---|
宿主 | Rabbit |
別名 | HADHA;ECHA;GBP;HADH;LCEH;LCHAD;MTPA;TP-ALPHA |
應用 | WB |
稀釋比例 | WB 1:500-2000. |
交叉反應 | Human Mouse Rat |
蛋白分子量 | 83kDa |
Gene ID | 3030 |
保存 | Store at -20°C. Avoid freeze / thaw cycles. |
儲存液 | Buffer: PBS with 0.03% Proclin300, 50% glycerol, pH7.3. |
純化方法 | Affinity purification |
亞型 | IgG |
免疫原 | Recombinant protein of human HADHA |
性狀 | 液體 |
Public Immunogen Range | Recombinant protein of human HADHA |
Subcellular Locations | Cytoplasm |
Swiss Prot | P40939 |
克隆類型 | Polyclonal Antibody |
背景資料 | This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. |